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KMID : 0605920020080020143
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Journal of Korean Association of Pediatric Surgeons
2002 Volume.8 No. 2 p.143 ~ p.155
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Biliary Atresia in Korea: A Survey by the Korean Association of Pediatric Surgeons
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Choi Kum-Ja
Kim Seong-Cheol
Kim Shin-Gon
Kim Woo-Ki
Kim In-Gu
Kim Jai-Eok
Kim Jae-Cheon
Kim Hae-Yeong
Kim Hyun-Hahk
Park Kwi-Won
Park Woo-Hyun
Song Young-Tack
Oh Soo-Myung
Lee Doo-Sun
Lee Myung-Duk
Lee Suk-Koo
Lee Sung-Cheol
Jung Sang-Young
Jung Sung-Eun
Jung Poong-Man
Chio Soon-Ok
Choi Seung-Hoon
Han Seok-Joo
Heo Young-Soo
Hong Jeong
Hwang Eui-Ho
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Abstract
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A survey on biliary atresia was made among 26 members of the Korean Association of Pediatric Surgeons. The members were required to complete a questionnaire and a case registration form for each patient during the twentyone-year period of 1980-2000. Three hundred and eighty patients were registered from 18 institutions. The average number of patients per surgeon was one to two every year. The male to female ratio was 1 : 1.3. The age of patients on diagnosis with biliary atresia was on average 65.4 +/-36.2 days old. The national distribution was 32.8% in Seoul, 25.3% in Gyoungki-Do, 21.6% in Gyoungsang-Do, 9.27% in Choongchung-Do, etc. in order. The most common clinical presentation was jaundice (98.4%) and change of stool color (86.2%) was second. Two hundred eighty (74.7%) of 375 patients were operated by 80 days of age. Three hundred thirty six (91.9%) of 366 patients were operated on by the original Kasai procedure, and 305 (84.3%) of 362 patients were observed by bile-drainage postoperatively. The overall postoperative complication rate was 18.5% and the overall postoperative mortality rate was 6.8%. The associated anomalies were observed in 72 cases (22.5%). One hundred ninty five (64.7%) of 302 patients have been alive in follow-up and 49 (25.1%) have survived over 5 years without problem after operation. Ascending cholangitis, varices and ascites affected survival significantly, and the important long-term prognostic factor was the occurrence of complications.
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KEYWORD
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Biliary atresia, National survey, Koreal
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